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126550-86-5

126550-86-5 Structure

126550-86-5 Structure
IdentificationBack Directory
[Name]

ALPHA-D-GAL-[1->4]-BETA-D-GAL-[1->4]-BETA-D-GLC-1->O-SPHINGOSINE
[CAS]

126550-86-5
[Synonyms]

Lysogb3
GLOBOTRIAOSYLSPHINGOSINE
Lyso-Globotriaosylceramide
globotriaosyl lysosphingolipid
Lyso-Globotriaosylceramide (d18:1)
Globotriaosylceramid?e Sphingosine
Globotriaosylsphingosine from porcine blood
α-d-gal-(1→4)-β-d-gal-(1→4)-β-d-glc-1→o-sphingosine
ALPHA-D-GAL-[1->4]-BETA-D-GAL-[1->4]-BETA-D-GLC-1->O-SPHINGOSINE
lyso-Ceramide trihexoside, metabolite of globotriaosylsphingosine
lyso-CeraMide Trihexoside (lyso-CTH, Globotriosyl sphingosine) Porcine
β-D-Glucopyranoside, (2S,3R,4E)-2-amino-3-hydroxy-4-octadecen-1-yl O-α-D-galactopyranosyl-(1→4)-O-β-D-galactopyranosyl-(1→4)-
[Molecular Formula]

C36H67NO17
[MDL Number]

MFCD00675433
[MOL File]

126550-86-5.mol
[Molecular Weight]

785.91
Chemical PropertiesBack Directory
[Boiling point ]

1005.8±65.0 °C(Predicted)
[density ]

1.37±0.1 g/cm3(Predicted)
[storage temp. ]

−20°C
[solubility ]

Chloroform:Methanol:Water (4:3:1): Soluble
[form ]

A solid
[pka]

11.74±0.45(Predicted)
[color ]

White to off-white
[InChIKey]

GRGNVOCPFLXGDQ-TWHXEDJUSA-N
[SMILES]

O[C@H]1[C@H](OC[C@H](N)[C@H](O)/C=C/CCCCCCCCCCCCC)O[C@H](CO)[C@@H](O[C@@H]2O[C@H](CO)[C@@H]([C@H](O)[C@H]2O)O[C@H]3O[C@H](CO)[C@@H]([C@H](O)[C@H]3O)O)[C@@H]1O
Safety DataBack Directory
[WGK Germany ]

3
[Storage Class]

11 - Combustible Solids
Hazard InformationBack Directory
[Uses]

Globotriaosylceramid?e Sphingosine tert-Butyldimethylsilyl is a Fabry disease biomarker.
[Biological Activity]

Globotriaosylsphingosine (Lyso GB3) is a potential biomarker of Fabry disease.
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