| Identification | Back Directory | [Name]
ALPHA-D-GAL-[1->4]-BETA-D-GAL-[1->4]-BETA-D-GLC-1->O-SPHINGOSINE | [CAS]
126550-86-5 | [Synonyms]
Lysogb3 GLOBOTRIAOSYLSPHINGOSINE Lyso-Globotriaosylceramide globotriaosyl lysosphingolipid Lyso-Globotriaosylceramide (d18:1) Globotriaosylceramid?e Sphingosine Globotriaosylsphingosine from porcine blood α-d-gal-(1→4)-β-d-gal-(1→4)-β-d-glc-1→o-sphingosine ALPHA-D-GAL-[1->4]-BETA-D-GAL-[1->4]-BETA-D-GLC-1->O-SPHINGOSINE lyso-Ceramide trihexoside, metabolite of globotriaosylsphingosine lyso-CeraMide Trihexoside (lyso-CTH, Globotriosyl sphingosine) Porcine β-D-Glucopyranoside, (2S,3R,4E)-2-amino-3-hydroxy-4-octadecen-1-yl O-α-D-galactopyranosyl-(1→4)-O-β-D-galactopyranosyl-(1→4)- | [Molecular Formula]
C36H67NO17 | [MDL Number]
MFCD00675433 | [MOL File]
126550-86-5.mol | [Molecular Weight]
785.91 |
| Chemical Properties | Back Directory | [Boiling point ]
1005.8±65.0 °C(Predicted) | [density ]
1.37±0.1 g/cm3(Predicted) | [storage temp. ]
−20°C | [solubility ]
Chloroform:Methanol:Water (4:3:1): Soluble | [form ]
A solid | [pka]
11.74±0.45(Predicted) | [color ]
White to off-white | [InChIKey]
GRGNVOCPFLXGDQ-TWHXEDJUSA-N | [SMILES]
O[C@H]1[C@H](OC[C@H](N)[C@H](O)/C=C/CCCCCCCCCCCCC)O[C@H](CO)[C@@H](O[C@@H]2O[C@H](CO)[C@@H]([C@H](O)[C@H]2O)O[C@H]3O[C@H](CO)[C@@H]([C@H](O)[C@H]3O)O)[C@@H]1O |
| Hazard Information | Back Directory | [Uses]
Globotriaosylceramid?e Sphingosine tert-Butyldimethylsilyl is a Fabry disease biomarker. | [Biological Activity]
Globotriaosylsphingosine (Lyso GB3) is a potential biomarker of Fabry disease. |
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