CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE

Request For Quotation
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Suppliers list
Company Name: Sigma-Aldrich  
Tel: 021-61415566 800-8193336
Email: orderCN@merckgroup.com
Company Name: Creative Enzymes  
Tel: 1-516-855-7709
Email: info@creative-enzymes.com
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Basic information
Product Name:CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE
Synonyms:EC 2.1.3.3;CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE;ORNITHINE TRANSCARBAMYLASE;ORNITHINE CARBAMYLTRANSFERASE;ornithine carbamoyl transferase from strept. faec.;ornithine carbamyltransferase from*streptococcus;Carbamoyltransferase, ornithine;ORNITHINE CARBAMYLTRANSFERASE FROM*STREP TOCOCCUS FA
CAS:9001-69-8
MF:
MW:0
EINECS:232-625-1
Product Categories:
Mol File:Mol File
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Structure
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Chemical Properties
storage temp. −20°C
form lyophilized powder
Specific Activity≥300units/mg protein
Safety Information
WGK Germany 3
Storage Class11 - Combustible Solids
MSDS Information
ProviderLanguage
SigmaAldrich English
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Usage And Synthesis
DescriptionAn enzyme that catalyzes the transfer of a carbamyl group from carbamyl phosphate to ornithine to form citrulline; it is a constituent reaction of the urea cycle. This enzyme normally occurs in the mitochondria of liver cells, but only to a minute extent in serum. Since it does not occur to a significant extent in serum, kidney, brain, etc., and only 1% or 2% of the hepatic concentration occurs in small intestine, its presence in serum is a specific indica_x0002_tion of damage to liver cells.
Biochem/physiol ActionsMutations in ornithine transcarbamylase cause Ornithine transcarbamylase deficiency which prevents the clearance of the byproduct ammonia leading to hyperammonemia.
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Preparation Products And Raw materials
Tag:CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE(9001-69-8) Related Product Information
2,4-Pentanedione, silver derivative N-Butylisocyanide Methyl isocyanoacetate 1,1,3,3-Tetramethylbutyl isocyanide tert-Butyl isocyanide Phenylselenol Ferric acetylacetonate SALCOMINE Benzyl isocyanide COBALT(II) ACETYLACETONATE Aluminum acetylacetonate Tosylmethyl isocyanide Cupric acetylacetonate Tris(2,4-pentanedionato)chroMiuM(III) Ethyl isocyanoacetate Tris(2,2,6,6-tetramethyl-3,5-heptanedionato)europium(III) Tris(2,2,6,6-tetramethyl-3,5-heptanedionato)dysprosium(III) Dichloro(ethylenediamine)platinum(II)