CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE
- CAS No.
- 9001-69-8
- Chemical Name:
- CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE
- Synonyms
- OTCase;EC 2.1.3.3;ORNITHINE TRANSCARBAMYLASE;ORNITHINE CARBAMYLTRANSFERASE;Carbamoyltransferase, ornithine;ornithine carbamyltransferase from*streptococcus;ornithine carbamoyl transferase from strept. faec.;CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE;ORNITHINE CARBAMYLTRANSFERASE FROM*STREP TOCOCCUS FA;Native Streptococcus faecalis Ornithine Transcarbamylase
- CBNumber:
- CB4174859
- Molecular Formula:
- Molecular Weight:
- 0
- MDL Number:
- MFCD00131769
- MOL File:
- Mol file
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE price More Price(1)
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Chemical Properties, Uses, Production
Description
An enzyme that catalyzes the transfer of a carbamyl group from carbamyl phosphate to ornithine to form citrulline; it is a constituent reaction of the urea cycle. This enzyme normally occurs in the mitochondria of liver cells, but only to a minute extent in serum. Since it does not occur to a significant extent in serum, kidney, brain, etc., and only 1% or 2% of the hepatic concentration occurs in small intestine, its presence in serum is a specific indica_x0002_tion of damage to liver cells.
Biochem/physiol Actions
Mutations in ornithine transcarbamylase cause Ornithine transcarbamylase deficiency which prevents the clearance of the byproduct ammonia leading to hyperammonemia.
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Preparation Products And Raw materials
Raw materials
Preparation Products
CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Suppliers
| Supplier | Tel | Country | ProdList | Advantage | |
|---|---|---|---|---|---|
| Sigma-Aldrich | 021-61415566 800-8193336 | orderCN@merckgroup.com | China | 51389 | 80 |
| Creative Enzymes | 1-516-855-7709 | info@creative-enzymes.com | United States | 8748 | 58 |
| Supplier | Advantage |
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| Sigma-Aldrich | 80 |
| Creative Enzymes | 58 |




