|
|
| | C18 Globotriaosylceramide-d3 (d18:1/18:0-d3) Basic information |
| | C18 Globotriaosylceramide-d3 (d18:1/18:0-d3) Chemical Properties |
| solubility | Chloroform: Methanol: (2:1): soluble DMSO: soluble |
| | C18 Globotriaosylceramide-d3 (d18:1/18:0-d3) Usage And Synthesis |
| Description | C18 Globotriaosylceramide-d3 is intended for use as an internal standard for the quantification of C18 globotriaosylceramide by GC- or LC-MS. C18 globotriaosylceramide is an endogenous sphingolipid that accumulates in the brain, heart, kidney, liver, lung, and spleen in a mouse model of Fabry disease, a lysosomal storage disorder characterized by a deficiency in the enzyme α-galactosidase A.1 As this product is derived from a natural source, there may be variations in the sphingoid backbone. [Matreya, LLC. Catalog No. 1537]WARNING This product is not for human or veterinary use. | | References | [1] MUSTAFA A KAMANI. Glycosphingolipid storage in Fabry mice extends beyond globotriaosylceramide and is affected by ABCB1 depletion[J]. Future Science OA, 2016, 2 1. DOI: 10.4155/fsoa-2016-0027 |
| | C18 Globotriaosylceramide-d3 (d18:1/18:0-d3) Preparation Products And Raw materials |
|